https://dx.doi.org/10.2196/publichealth.5516">
 

Abstract

Background: Owing to their low prevalence, single rare conditions are difficult to monitor through current state passive and active case ascertainment systems. However, such monitoring is important because, as a group, rare conditions have great impact on the health of affected individuals and the well-being of their caregivers. A viable approach could be to conduct passive and active case ascertainment of several rare conditions simultaneously. This is a report about the feasibility of such an approach.

Objective: To test the feasibility of a case ascertainment system with passive and active components aimed at monitoring 3 rare conditions simultaneously in 3 states of the United States (Colorado, Kansas, and South Carolina). The 3 conditions are spina bifida, muscular dystrophy, and fragile X syndrome.

Methods: Teams from each state evaluated the possibility of using current or modified versions of their local passive and active case ascertainment systems and datasets to monitor the 3 conditions. Together, these teams established the case definitions and selected the variables and the abstraction tools for the active case ascertainment approach. After testing the ability of their local passive and active case ascertainment system to capture all 3 conditions, the next steps were to report the number of cases detected actively and passively for each condition, to list the local barriers against the combined passive and active case ascertainment system, and to describe the experiences in trying to overcome these barriers.

Results: During the test period, the team from South Carolina was able to collect data on all 3 conditions simultaneously for all ages. The Colorado team was also able to collect data on all 3 conditions but, because of age restrictions in its passive and active case ascertainment system, it was able to report few cases of fragile X syndrome. The team from Kansas was able to collect data only on spina bifida. For all states, the implementation of an active component of the ascertainment system was problematic. The passive component appears viable with minor modifications.

Conclusions: Despite evident barriers, the joint passive and active case ascertainment of rare disorders using modified existing surveillance systems and datasets seems feasible, especially for systems that rely on passive case ascertainment.

Department

Institute on Disability

Publication Date

8-29-2016

Journal Title

JMIR Public Health and Surveillance

Publisher

JMIR Publications

Digital Object Identifier (DOI)

https://dx.doi.org/10.2196/publichealth.5516

Document Type

Article

Rights

©Amanda Reichard, Suzanne McDermott, Margaret Ruttenber, Joshua Mann, Michael G Smith, Julie Royer, Rodolfo Valdez. Originally published in JMIR Public Health and Surveillance (http://publichealth.jmir.org), 29.08.2016.

Comments

This is an article published by JMIR Publications in JMIR Public Health and Surveillance in 2016, available online: https://dx.doi.org/10.2196/publichealth.5516

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